Type: | Family | Name: | Succinylglutamate desuccinylase/aspartoacylase |
Description: | This family describes both succinylglutamate desuccinylase that catalyses the fifth and last step in arginine catabolism by the arginine succinyltransferase pathway and also includes aspartoacylase which cleaves acylaspartate into a fatty acid and aspartate. Mutations in lead to Canavan disease []. | Short Name: | Aste_AspA |